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KMID : 0363220140520030169
Korean Journal of Dermatology
2014 Volume.52 No. 3 p.169 ~ p.172
Juvenile Dermatomyositis Presenting as Deep Skin Ulcerations as an Initial Manifestation
Kwon Sun-Yong

Chae Jin-Kyung
Park Sang-Hyun
Ko Joo-Yeon
Park Seok-Don
Park Kun
Abstract
Juvenile dermatomyositis is a common idiopathic inflammatory myopathy in childhood and is characterized by symmetric proximal muscle weakness and specific cutaneous manifestations. We here report on a 12-year-old boy who presented with violaceous maculopatches with multiple deep skin ulcerations on the right arm and lower back 4 months ago. One month after the initial visit, he had difficulty climbing stairs and elevating his arms above the head. Laboratory tests showed elevation of the serum levels of skeletal muscle enzymes, and electromyogram and muscle biopsy indicated myopathy. Histopathological analysis of the ulceration indicated necrotizing vasculitis and calcification. Based on these findings, his condition was diagnosed as juvenile dermatomyositis. We believe that this case is unique because of the difficulty in diagnosing the condition, as skin ulceration is a rare cutaneous manifestation of dermatomyositis.
KEYWORD
Juvenile dermatomyositis, Skin ulceration
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